NCT04061512

Brief Summary

Waldenström's macroglobulinaemia (WM) is a rare type of slow growing lymphoma. It develops when white blood cells grow abnormally. Typically a disease of the elderly, the median age of presentation is \>70 years and the current treatment for WM is unsatisfactory, with incomplete responses and inevitable recurrence. Therefore there is a need to find alternative treatments that are more effective, leading to lasting responses and improved quality of life. The RAINBOW study is a phase 2-3 trial assessing 'chemotherapy free' treatment as primary therapy for WM which can potentially improve response outcome, durability and importantly, reduce toxicity for WM patients. This approach will be done using the drug Ibrutinib, which in combination with rituximab (RI) will be the experimental arm. As there is no agreed standard on first-line therapy for WM, the control arm is the current treatment based on the most recently published clinical trial results. The control arm consists of rituximab, cyclophosphamide and dexamethasone (DCR), and is widely recommended by international consensus as appropriate treatment for first-line therapy for WM. In this study, 148 adults (aged ≥ 18 years) with treatment naïve WM will be randomised on a 1:1 ratio to either the treatment or control arm. Randomised treatment lasts for a maximum of 6 cycles and response will be assessed following 3 cycles of treatment and completion of randomised treatment at approximately 24 weeks after commencing treatment. RI patients may then have up to 5 years of Ibrutinib monotherapy. Patients will be seen regularly during treatment and then every 3 months for 5 years after treatment discontinuation. Patients will enter annual follow up for survival until the end of trial (including progressed patients). The study will be conducted at NHS hospitals and is expected to last 9 years and 6 months.

Trial Health

77
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
148

participants targeted

Target at P75+ for phase_2

Timeline
46mo left

Started Feb 2020

Longer than P75 for phase_2

Geographic Reach
1 country

25 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress63%
Feb 2020Mar 2030

First Submitted

Initial submission to the registry

July 1, 2019

Completed
2 months until next milestone

First Posted

Study publicly available on registry

August 19, 2019

Completed
6 months until next milestone

Study Start

First participant enrolled

February 3, 2020

Completed
10.1 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

March 1, 2030

Expected
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

March 1, 2030

Last Updated

May 10, 2024

Status Verified

May 1, 2024

Enrollment Period

10.1 years

First QC Date

July 1, 2019

Last Update Submit

May 9, 2024

Conditions

Outcome Measures

Primary Outcomes (2)

  • Percentage of patients achieving a preliminary efficacy (response) of the 'chemotherapy free' combination of rituximab and ibrutinib (RI) as primary therapy for WM.

    Overall response rate at week 24

  • Progression free survival (PFS) analysis of rituximab/ibrutinib (RI) when compared to dexamethasone/rituximab/cyclophosphamide (DRC) at 2 years after the last randomisation

    2 years after the last randomisation

Secondary Outcomes (6)

  • Safety and tolerability of RI compared to DRC assessed by the frequency of serious and non-serious adverse events according to CTCAE v5.0

    until 30 calendar days post last IMP administration

  • Overall response rate (defined as complete response [CR], very good partial response [VGPR], partial response [PR] and minor response [MR]) of RI compared to DRC (at end of randomised treatment and best response over any time point)

    through study completion, an average of 2 years.

  • Time to next treatment

    through study completion, an average of 2 years.

  • Duration of response of RI compared to DRC

    through study completion, an average of 2 years.

  • Overall survival (OS) of patients treated with RI compared to DRC

    date of randomisation until the date of death (of any cause)

  • +1 more secondary outcomes

Study Arms (2)

DRC Arm

ACTIVE COMPARATOR

The DRC arm (chemotherapy) is the control arm and consists of rituximab, cyclophosphamide and dexamethasone. It is widely recommended by international consensus as appropriate treatment for first-line therapy for WM.

Drug: Dexamethasone, cyclophosphamide, rituximab

RI Arm

EXPERIMENTAL

The RI arm (chemotherapy free) arm will be using the drug ibrutinib, which in combination with rituximab (RI) will be the experimental arm.

Drug: Rituximab, ibrutinib

Interventions

DRC Arm (chemotherapy) consists of dexamethasone, cyclophosphamide and rituximab treatment

DRC Arm

RI Arm (chemotherapy free) consists of rituximab and ibrutinib treatment

RI Arm

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Patients ≥ 18 years
  • Confirmed diagnosis of WM (according to consensus panel / WHO criteria) with measurable IgM paraprotein
  • Previously untreated disease at any stage requiring therapy at the discretion of the treating physician. Suggested criteria for initiating treatment include:
  • haematological suppression to Hb \<10g/dl, or neutrophils \<1.5x109/l or platelets \<150x109/l
  • clinical evidence of hyperviscosity
  • bulky lymphadenopathy and/or bulky splenomegaly
  • presence of B symptoms
  • No previous chemotherapy (prior plasma exchange and steroids are permissible)
  • Eastern Cooperative Oncology Group (ECOG) performance status grade 0 - 2
  • Life expectancy of greater than 6 months
  • Written informed consent
  • Willing to comply with the contraceptive requirements of the trial
  • Negative serum or urine pregnancy test for women of childbearing potential (WOCBP)

You may not qualify if:

  • Prior therapy for WM
  • Lymphoplasmacytic lymphoma with no detectable serum IgM paraprotein
  • CNS involvement with WM
  • Autoimmune cytopenias
  • Major surgery within 4 weeks prior to randomisation
  • Clinically significant cardiac disease including the following:
  • Myocardial infarction within 6 months prior to randomisation
  • Unstable angina within 3 months prior to randomisation
  • New York Heart Association class III or IV congestive heart failure
  • History of clinically significant arrhythmias (e.g. sustained ventricular tachycardia, ventricular fibrillation, torsades de pointes)
  • QTcF \> 480 msecs based on Fredericia's formula or Bazette's formula
  • History of Mobitz II second degree or third degree heart block without a permanent pacemaker in place
  • Uncontrolled hypertension as indicated by a minimum of 2 consecutive blood pressure measurements showing systolic blood pressure \> 170 mmHg and diastolic blood pressure \> 105 mm Hg
  • Cardiac event within 6 months of screening (e.g. coronary artery stent) requiring dual antiplatelet treatment
  • History of stroke or intracranial haemorrhage within 6 months prior to randomisation
  • +19 more criteria

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (25)

Royal United Hospital, Bath

Bath, United Kingdom

RECRUITING

The Royal Bournemouth and Christchurch Hospitals NHS Foundation Trust

Bournemouth, United Kingdom

RECRUITING

East Kent Hospitals University NHS Foundation Trust

Canterbury, United Kingdom

RECRUITING

University Hospital of Wales

Cardiff, United Kingdom

RECRUITING

Colchester Hospital

Colchester, United Kingdom

RECRUITING

Mid Yorkshire NHS Trust

Dewsbury, United Kingdom

RECRUITING

Royal Devon University Hospital

Exeter, United Kingdom

RECRUITING

Medway Maritime Hospital

Gillingham, United Kingdom

RECRUITING

Castle Hill Hospital

Hull, United Kingdom

RECRUITING

NHS Lanarkshire

Lanark, United Kingdom

RECRUITING

St James's University Hospital

Leeds, United Kingdom

RECRUITING

Leicester Royal Infirmary

Leicester, United Kingdom

RECRUITING

Barking, Havering and Redbridge University Hospitals NHS Trust

London, United Kingdom

RECRUITING

Barts Health NHS Trust

London, United Kingdom

RECRUITING

King's College Hospital

London, United Kingdom

RECRUITING

Northwick Park Hospital

London, United Kingdom

RECRUITING

University College London Hospitals NHS Foundation Trust

London, United Kingdom

RECRUITING

Christie NHS Foundation Trust

Manchester, United Kingdom

RECRUITING

Norfolk and Norwich Hospital

Norwich, United Kingdom

RECRUITING

Oxford University Hospital

Oxford, United Kingdom

RECRUITING

University Hospitals Plymouth NHS Trust

Plymouth, United Kingdom

RECRUITING

Salisbury NHS Foundation Trust

Salisbury, United Kingdom

RECRUITING

Torbay & Newton Abbot Hospital

Torquay, United Kingdom

RECRUITING

Royal Cornwall Hospital

Truro, United Kingdom

RECRUITING

Hampshire Hospitals NHS Foundation Trust

Winchester, United Kingdom

RECRUITING

MeSH Terms

Conditions

Waldenstrom Macroglobulinemia

Interventions

DexamethasoneCyclophosphamideRituximabibrutinib

Condition Hierarchy (Ancestors)

Neoplasms, Plasma CellNeoplasms by Histologic TypeNeoplasmsHemostatic DisordersVascular DiseasesCardiovascular DiseasesParaproteinemiasBlood Protein DisordersHematologic DiseasesHemic and Lymphatic DiseasesHemorrhagic DisordersLymphoproliferative DisordersLymphatic DiseasesImmunoproliferative DisordersImmune System Diseases

Intervention Hierarchy (Ancestors)

PregnadienetriolsPregnadienesPregnanesSteroidsFused-Ring CompoundsPolycyclic CompoundsSteroids, FluorinatedPhosphoramide MustardsNitrogen Mustard CompoundsMustard CompoundsHydrocarbons, HalogenatedHydrocarbonsOrganic ChemicalsPhosphoramidesOrganophosphorus CompoundsAntibodies, Monoclonal, Murine-DerivedAntibodies, MonoclonalAntibodiesImmunoglobulinsImmunoproteinsBlood ProteinsProteinsAmino Acids, Peptides, and ProteinsSerum GlobulinsGlobulins

Central Study Contacts

RAINBOW Trial Coordinator

CONTACT

UCL CTC haematology trials team

CONTACT

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

July 1, 2019

First Posted

August 19, 2019

Study Start

February 3, 2020

Primary Completion (Estimated)

March 1, 2030

Study Completion (Estimated)

March 1, 2030

Last Updated

May 10, 2024

Record last verified: 2024-05

Data Sharing

IPD Sharing
Will not share

Locations