NCT03442764

Brief Summary

This is a multicenter, exploratory, randomized, double-blind study of the administration of mavacamten in 60 participants with symptomatic nHCM randomized to receive a 16-week course of mavacamten doses titrated to achieve 1 of 2 target drug concentrations.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
59

participants targeted

Target at P50-P75 for phase_2

Timeline
Completed

Started Mar 2018

Geographic Reach
1 country

32 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

February 9, 2018

Completed
13 days until next milestone

First Posted

Study publicly available on registry

February 22, 2018

Completed
1 month until next milestone

Study Start

First participant enrolled

March 30, 2018

Completed
1.8 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

January 7, 2020

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

January 7, 2020

Completed
2.6 years until next milestone

Results Posted

Study results publicly available

August 9, 2022

Completed
Last Updated

August 9, 2022

Status Verified

July 1, 2022

Enrollment Period

1.8 years

First QC Date

February 9, 2018

Results QC Date

May 27, 2022

Last Update Submit

July 14, 2022

Conditions

Outcome Measures

Primary Outcomes (2)

  • Percentage of Participants Who Experienced at Least One Treatment Emergent Adverse Event (TEAE)

    This is the percentage of participants who experienced at least one treatment emergent adverse event (TEAE)

    From first dose to 8 weeks following last dose (Up to 24 weeks)

  • Percentage of Participants Who Experienced at Least One Serious Treatment-emergent Adverse Event (STEAE)

    This is the percentage of participants who experienced at least one serious treatment-emergent adverse event (STEAE)

    From first dose to 8 weeks following last dose (Up to 24 weeks)

Study Arms (3)

Group 1

EXPERIMENTAL

Active Treatment for participants with base target trough concentration

Drug: mavacamten

Group 2

EXPERIMENTAL

Active Treatment for participants with higher target trough concentration

Drug: mavacamten

Placebo

PLACEBO COMPARATOR

Placebo Group

Drug: Placebo

Interventions

MYK-461

Also known as: MYK-461
Group 1Group 2

Placebo

Placebo

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Diagnosed with nHCM (hypertrophied and non-dilated left ventricle in absence of systemic or other known cause), with LV wall thickness ≥ 15mm at Screening or ≥ 13mm with a positive family history of HCM.
  • Age 18 and greater, Body weight \> 45kg
  • Documented LVEF ≥ 55% at the Screening as determined by echo central lab
  • LVOT gradient \< 30 mmHg at rest AND during Valsalva AND post-exercise
  • NYHA functional class II or III
  • Elevated NT-proBNP at rest

You may not qualify if:

  • History of syncope, sustained ventricular tachyarrhythmia with exercise, obstructive coronary artery disease or myocardial infarction within the past 6 months
  • History of resuscitated sudden cardiac arrest at any time or known appropriate implantable cardioverter defibrillator (ICD) discharge within 6 months prior to Screening
  • Current treatment with disopyramide or ranolazine (within 14 days prior to Screening)
  • Current or planned treatment during the study with a combination of beta-blockers and calcium channel blockers
  • Has been treated with invasive septal reduction (surgical myectomy or percutaneous alcohol septal ablation \[ASA\]) within 6 months prior to Screening
  • History of resting or post-exercise LVOT \>30 mmHg unless subsequently treated by septal reduction
  • Has QTc Fridericia (QTcF) \>480 ms or any other ECG abnormality considered by the investigator to pose a risk to participant safety (eg, second-degree atrioventricular block type II)
  • Has persistent or permanent atrial fibrillation not on anticoagulation for at least 4 weeks prior to Screening and/or not adequately rate-controlled within 1 year of Screening
  • History of clinically significant malignant disease within 10 years such as non-metastatic cutaneous squamous cell or basal cell carcinoma
  • History or evidence of any other clinically significant disorder, condition, or disease that, in the opinion of the investigator or MyoKardia physician, would pose a risk to subject safety or interfere with the study evaluation, procedures, or completion.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (32)

Mayo Clinic Arizona

Scottsdale, Arizona, 85259, United States

Location

Cedars-Sinai Medical Center (Smidt Heart Institute)

Los Angeles, California, 90048, United States

Location

Stanford Hospital and Clinics/Stanford University

Palo Alto, California, 94305, United States

Location

University of California, San Francisco

San Francisco, California, 94143, United States

Location

Yale New Haven Hospital

New Haven, Connecticut, 06520, United States

Location

Northwestern University

Evanston, Illinois, 60208, United States

Location

St. Vincent Medical Group

Indianapolis, Indiana, 46260, United States

Location

University of Iowa Hospitals and clinics

Iowa City, Iowa, 52242, United States

Location

University of Maryland Medical System

Baltimore, Maryland, 21201, United States

Location

Brigham and Women's Hospital

Boston, Massachusetts, 02115, United States

Location

Michigan Medicine

Ann Arbor, Michigan, 48109, United States

Location

Henry Ford Hospital

Detroit, Michigan, 48202, United States

Location

Washington University School of Medicine

St Louis, Missouri, 63110, United States

Location

NYU Winthrop Hospital

Mineola, New York, 11501, United States

Location

NYU Langone Medical Center

New York, New York, 10016, United States

Location

Carolinas Medical Center

Charlotte, North Carolina, 28203, United States

Location

Duke Cardiology at Southpoint

Durham, North Carolina, 27713, United States

Location

University of Cincinnati Medical Center

Cincinnati, Ohio, 45219, United States

Location

Oregon Health and Science University

Portland, Oregon, 97239, United States

Location

St. Luke's Cardiology Associates

Bethlehem, Pennsylvania, 18018, United States

Location

Penn State Health Milton S. Hershey Medical Center

Hershey, Pennsylvania, 17033-0850, United States

Location

University of Pennsylvania

Philadelphia, Pennsylvania, 19104, United States

Location

UPMC Presbyterian

Pittsburgh, Pennsylvania, 15213, United States

Location

The University of Texas Southwestern Medical Center at Dallas

Dallas, Texas, 75390-9034, United States

Location

Baylor St. Luke Medical Center at Houston, Texas Heart Institute Out-patient Clinic

Houston, Texas, 77030, United States

Location

Houston Methodist Hospital

Houston, Texas, 77030, United States

Location

Intermountain Medical Center

Murray, Utah, 84107, United States

Location

University of Utah Medical Center

Salt Lake City, Utah, 84132, United States

Location

University of Virginia

Charlottesville, Virginia, 22908, United States

Location

Virginia Commonwealth University

Richmond, Virginia, 23298, United States

Location

University of Washington Medical Center

Seattle, Washington, 98195, United States

Location

Unity Point Health Meriter Heart and Vascular Institute

Madison, Wisconsin, 53713, United States

Location

Related Publications (1)

  • Ho CY, Mealiffe ME, Bach RG, Bhattacharya M, Choudhury L, Edelberg JM, Hegde SM, Jacoby D, Lakdawala NK, Lester SJ, Ma Y, Marian AJ, Nagueh SF, Owens A, Rader F, Saberi S, Sehnert AJ, Sherrid MV, Solomon SD, Wang A, Wever-Pinzon O, Wong TC, Heitner SB. Evaluation of Mavacamten in Symptomatic Patients With Nonobstructive Hypertrophic Cardiomyopathy. J Am Coll Cardiol. 2020 Jun 2;75(21):2649-2660. doi: 10.1016/j.jacc.2020.03.064.

MeSH Terms

Interventions

MYK-461

Results Point of Contact

Title
Bristol-Myers Squibb Study Director
Organization
Bristol-Myers Squibb

Study Officials

  • Myokardia Medical Information Team

    MyoKardia, Inc.

    STUDY DIRECTOR

Publication Agreements

PI is Sponsor Employee
No
Restrictive Agreement
No

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

February 9, 2018

First Posted

February 22, 2018

Study Start

March 30, 2018

Primary Completion

January 7, 2020

Study Completion

January 7, 2020

Last Updated

August 9, 2022

Results First Posted

August 9, 2022

Record last verified: 2022-07

Locations