NCT03197688

Brief Summary

The Opsumit Users registry (OPUS; NCT02126943) was developed to characterize the safety profile of Opsumit and to describe clinical characteristics and outcomes of patients newly treated with Opsumit in the post-marketing setting. It is expected that the recruitment target of the OPUS registry cannot be achieved within the planned time period (5000 Opsumit new users by October 2018). The OrPHeUS study is designed to supplement the OPUS registry with retrospectively identified first-time Opsumit users in order to achieve the desired sample size.

Trial Health

90
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
2,200

participants targeted

Target at P75+ for all trials

Timeline
Completed

Started Aug 2017

Geographic Reach
2 countries

106 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

May 12, 2017

Completed
1 month until next milestone

First Posted

Study publicly available on registry

June 23, 2017

Completed
1 month until next milestone

Study Start

First participant enrolled

August 3, 2017

Completed
1.1 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

September 6, 2018

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

September 6, 2018

Completed
Last Updated

March 30, 2025

Status Verified

March 1, 2025

Enrollment Period

1.1 years

First QC Date

May 12, 2017

Last Update Submit

March 28, 2025

Conditions

Outcome Measures

Primary Outcomes (1)

  • Estimation of incidence rates of adverse events

    Incidence rates of liver test abnormalities, Occurrence of Hepatic Adverse Events (HAEs), Occurrence of any other Adverse Event (AE), Occurrence and reason for discontinuation of Opsumit treatment, hospitalization and death

    Observation period from 19 Oct 2013 to 31 March 2017, Data collection from 1 Apr 2017 to 30 Jun 2018

Secondary Outcomes (2)

  • Description of demographic characteristics of patients

    Observation period from 19 Oct 2013 to 31 March 2017, Data collection from 1 Apr 2017 to 30 Jun 2018

  • Description of clinical characteristics of patients

    Observation period from 19 Oct 2013 to 31 March 2017, Data collection from 1 Apr 2017 to 30 Jun 2018

Study Arms (1)

Notapplicable

Not applicable as non-interventional study

Other: Notapplicable

Interventions

Not applicable as non-interventional study

Notapplicable

Eligibility Criteria

Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)
Sampling MethodNon-Probability Sample
Study Population

Patients who initiated Opsumit for the first time between 19 October 2013 and 31 December 2016 (inclusive) are eligible for OrPHeUS (i.e., eligibility period).

You may qualify if:

  • Patients who initiated Opsumit for the first time between 19 October 2013 and 31 December 2016 (inclusive)
  • Patients whose medical charts are available for data collection

You may not qualify if:

  • Patient participation in the OPUS registry
  • Patient participation in any clinical trial involving Opsumit treatment or macitentan investigational product

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (106)

Pulmonary Associates

Phoenix, Arizona, 85006, United States

Location

Cardiovascular Consultants

Phoenix, Arizona, 85032, United States

Location

Mayo Clinic - Arizona

Phoenix, Arizona, 85054, United States

Location

University of California San Diego

La Jolla, California, 93093, United States

Location

Loma Linda University Medical Center

Loma Linda, California, 92354, United States

Location

University of Southern California

Los Angeles, California, 90033, United States

Location

David Geffen School of Medicine at University of California Los Angeles

Los Angeles, California, 90095-1690, United States

Location

UCSF School of Medicine

San Francisco, California, 94143, United States

Location

Paloma Medical Group

San Juan Capistrano, California, 92675, United States

Location

Santa Barbara Cottage Hospital

Santa Barbara, California, 93105, United States

Location

University of Colorado

Aurora, Colorado, 80045, United States

Location

National Jewish Health

Denver, Colorado, 80206, United States

Location

Yale University

New Haven, Connecticut, 06520, United States

Location

Christiana Care Health Services

Newark, Delaware, 19718, United States

Location

MedStar Georgetown University Hospital

Washington D.C., District of Columbia, 20007, United States

Location

Bay Area Cardiology Associates

Brandon, Florida, 33511, United States

Location

Florida Lung, Asthma and Sleep Specialists

Celebration, Florida, 34747, United States

Location

Frank Hull, MD, PA

Fort Lauderdale, Florida, 33316, United States

Location

University of Florida

Gainesville, Florida, 32610, United States

Location

West Pasco Pulmonary Associates

Hudson, Florida, 34667, United States

Location

Saint Vincent's Medical Center

Jacksonville, Florida, 32209, United States

Location

Medical Research of Central Florida

Leesburg, Florida, 34748, United States

Location

Independent Lung Associates

Melbourne, Florida, 32901, United States

Location

University of Miami

Miami, Florida, 33136, United States

Location

Mount Sinai Comprehensive Cancer Center

Miami Beach, Florida, 33140, United States

Location

Central Florida Pulmonary Group, P.A. - Downtown Orlando Office

Orlando, Florida, 32803, United States

Location

Bassetti Medical Research Inc

Sebring, Florida, 33870, United States

Location

Cardiovascular Medicine Associates

South Miami, Florida, 33143, United States

Location

Coastal Pulmonary and Critical Care

St. Petersburg, Florida, 33704, United States

Location

University of South Florida

Tampa, Florida, 33606, United States

Location

Cleveland Clinic Florida Hospital

Weston, Florida, 33331, United States

Location

Florida Medical Clinic

Zephyrhills, Florida, 33542, United States

Location

Piedmont Healthcare

Austell, Georgia, 30106, United States

Location

Southeastern Cardiology Associates

Columbus, Georgia, 31904, United States

Location

Wellstar Marietta Pulmonary Medicine

Marietta, Georgia, 30060, United States

Location

Bingham Memorial Hospital

Shelley, Idaho, 83274, United States

Location

Northwestern University

Chicago, Illinois, 60611, United States

Location

IU Health Physicians Pulmonary & Critical Care

Carmel, Indiana, 46032, United States

Location

Lutheran Hospital

Fort Wayne, Indiana, 46804, United States

Location

Indiana Internal Medicine Consultants

Greenwood, Indiana, 46143, United States

Location

St. Vincent Medical Group, Inc.

Indianapolis, Indiana, 46260, United States

Location

CIC Associates

Clive, Iowa, 50325, United States

Location

University of Iowa Hospitals and Clinics

Iowa City, Iowa, 52242, United States

Location

The University of Kansas Physicians

Kansas City, Kansas, 66160, United States

Location

St. Elizabeth Healthcare Clinical Research Institute

Erlanger, Kentucky, 41018, United States

Location

Kentuckiana Pulmonary Associates

Louisville, Kentucky, 40202, United States

Location

LSU Health Sciences Center

New Orleans, Louisiana, 70112, United States

Location

Ochsner Medical Center

New Orleans, Louisiana, 70121, United States

Location

Pulmonary & Critical Care Specialists

Shreveport, Louisiana, 71105, United States

Location

Tufts Medical Center

Boston, Massachusetts, 02111, United States

Location

Massachusetts General Hospital

Boston, Massachusetts, 02114, United States

Location

Boston University Medical Center

Boston, Massachusetts, 02118, United States

Location

University of Michigan Medical Center

Ann Arbor, Michigan, 48109, United States

Location

Henry Ford Health System

Detroit, Michigan, 48202, United States

Location

Sparrow Clinical Research Institute

Lansing, Michigan, 48912, United States

Location

Beaumont Medical Center

Troy, Michigan, 48085, United States

Location

Minneapolis Heart Institute

Minneapolis, Minnesota, 55407-3799, United States

Location

University of Mississippi Medical Center

Jackson, Mississippi, 39216, United States

Location

Saint Louis University

St Louis, Missouri, 63104, United States

Location

Pulmonary Consultants Inc-St. Louis

St Louis, Missouri, 63136, United States

Location

Mercy Hospital Saint Louis

St Louis, Missouri, 63141, United States

Location

Nebraska Pulmonary Specialties, LLC

Lincoln, Nebraska, 68506, United States

Location

University of Nebraska Medical Center

Omaha, Nebraska, 68198-5990, United States

Location

Barnabas Health Ambulatory Care Center

Newark, New Jersey, 07112, United States

Location

Pulmonary and Critical Care Associates

Union, New Jersey, 07083, United States

Location

University of New Mexico

Albuquerque, New Mexico, 87131-0001, United States

Location

Albany Medical Center

Albany, New York, 12208, United States

Location

Pulmonary Health Physicians

Fayetteville, New York, 13066, United States

Location

Stony Brook University Hospital

Hauppauge, New York, 11788, United States

Location

Temple University Hospital

Middletown, New York, 10941, United States

Location

Winthrop University Hospital, Clinical Trials Center

Mineola, New York, 11501, United States

Location

Mount Sinai

New York, New York, 10029, United States

Location

Montefiore Medical Center - Bronx

The Bronx, New York, 10467, United States

Location

University of North Carolina Hospitals

Chapel Hill, North Carolina, 27599, United States

Location

Duke University Medical Center

Durham, North Carolina, 27710, United States

Location

University of Cincinnati

Cincinnati, Ohio, 45242, United States

Location

Ohio State University, Wexner Medical Center

Columbus, Ohio, 43210, United States

Location

Mount Carmel Medical Group

Columbus, Ohio, 43213, United States

Location

Midwest Pulmonary & Sleep Research

Dayton, Ohio, 45459, United States

Location

Southwest General Health Center

Middleburg Heights, Ohio, 44130, United States

Location

The University of Toledo Medical Center

Toledo, Ohio, 43614, United States

Location

Oklahoma Heart Hospital

Oklahoma City, Oklahoma, 73120, United States

Location

Oregon Health & Science University

Portland, Oregon, 97201-3098, United States

Location

Legacy Research Institute

Portland, Oregon, 97210, United States

Location

The Oregon Clinic

Portland, Oregon, 97225, United States

Location

Doylestown Health Cardiology, a division of Doylestown Health Physicians

Doylestown, Pennsylvania, 18907, United States

Location

University of Pennsylvania Health System

Philadelphia, Pennsylvania, 19104, United States

Location

Thomas Jefferson University

Philadelphia, Pennsylvania, 19107, United States

Location

Allegheny General Hospital

Pittsburgh, Pennsylvania, 15212, United States

Location

Lankenau Medical Center

Wynnewood, Pennsylvania, 19096, United States

Location

AnMed Health Medical Center

Anderson, South Carolina, 29621, United States

Location

Carolina Cardiology Associates

Rock Hill, South Carolina, 29732, United States

Location

Sioux Falls Cardiovascular PC

Sioux Falls, South Dakota, 57108, United States

Location

Memorial Research Center

Chattanooga, Tennessee, 37404, United States

Location

Mid-South Pulmonary Specialists

Memphis, Tennessee, 38157, United States

Location

University of Texas Southwestern Medical Center at Dallas

Dallas, Texas, 75390-8550, United States

Location

Premier Pulmonary CC and Sleep Medicine, PA

Denison, Texas, 75020, United States

Location

Houston Methodist Hospital

Houston, Texas, 77030, United States

Location

University of Texas Health Science Center at Houston

Houston, Texas, 77030, United States

Location

Baylor Regional Medical Center at Plano

Plano, Texas, 75093, United States

Location

Scott and White Memorial Hospital

Temple, Texas, 76508-0001, United States

Location

University of Washington

Seattle, Washington, 98195, United States

Location

Spokane Respiratory Consultants

Spokane, Washington, 99204-4800, United States

Location

Cardiac Study Center

Tacoma, Washington, 98405, United States

Location

Aurora Health Care - Saint Luke's Medical Center

Milwaukee, Wisconsin, 53215, United States

Location

CardioPulmonary Research Center

Guaynabo, 00968, Puerto Rico

Location

Related Publications (5)

  • Melendres-Groves LD, Channick RN, Chin KM, McLaughlin VV, MacDonald G, Martin N, Ong R, Sandros M, Kim NH. Characteristics, Treatment Patterns and Outcomes of Patients with Pulmonary Arterial Hypertension by Race and Ethnicity Using Real-World Data from the Combined OPUS/OrPHeUS Studies. Adv Ther. 2025 Nov 19. doi: 10.1007/s12325-025-03403-4. Online ahead of print.

  • Kim NH, Chin KM, McLaughlin VV, Ong R, MacDonald G, Martin N, Senatore A, Channick R. Macitentan and Tadalafil Combination Therapy in Patients with Pulmonary Arterial Hypertension and Cardiovascular Comorbidities: Real-World Evidence from OPUS and OrPHeUS. Adv Ther. 2025 Jul;42(7):3306-3333. doi: 10.1007/s12325-025-03180-0. Epub 2025 May 19.

  • Chin KM, Channick R, Kim NH, Ong R, Turricchia S, Martin N, Mitchell L, McLaughlin VV. Macitentan in Pulmonary Arterial Hypertension Due to Congenital Heart Disease (CHD-PAH): Real-World Evidence from the OPUS/OrPHeUS Studies. Cardiol Ther. 2024 Dec;13(4):775-796. doi: 10.1007/s40119-024-00386-1. Epub 2024 Nov 25.

  • Channick R, Chin KM, McLaughlin VV, Lammi MR, Zamanian RT, Turricchia S, Ong R, Mitchell L, Kim NH. Macitentan in Pulmonary Arterial Hypertension Associated with Connective Tissue Disease (CTD-PAH): Real-World Evidence from the Combined OPUS/OrPHeUS Dataset. Cardiol Ther. 2024 Jun;13(2):315-339. doi: 10.1007/s40119-024-00361-w. Epub 2024 Mar 7.

  • Kim NH, Chin KM, McLaughlin VV, DuBrock H, Restrepo-Jaramillo R, Safdar Z, MacDonald G, Martin N, Rosenberg D, Solonets M, Channick R. Safety of Macitentan for the Treatment of Portopulmonary Hypertension: Real-World Evidence from the Combined OPUS/OrPHeUS Studies. Pulm Ther. 2024 Mar;10(1):85-107. doi: 10.1007/s41030-023-00251-x. Epub 2024 Jan 7.

MeSH Terms

Conditions

Pulmonary Arterial Hypertension

Condition Hierarchy (Ancestors)

Hypertension, PulmonaryLung DiseasesRespiratory Tract Diseases

Study Design

Study Type
observational
Observational Model
COHORT
Time Perspective
RETROSPECTIVE
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

May 12, 2017

First Posted

June 23, 2017

Study Start

August 3, 2017

Primary Completion

September 6, 2018

Study Completion

September 6, 2018

Last Updated

March 30, 2025

Record last verified: 2025-03

Locations