NCT02597114

Brief Summary

AGT-181 is a fusion protein containing alpha-L-Iduronidase that is intended to deliver the enzyme peripherally and to the brain, when administered intravenously. This study is an extension of a safety and dose ranging study to obtain long term safety and exposure data, as well as information on the biological activity of the investigational drug

Trial Health

100
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
3

participants targeted

Target at below P25 for phase_1

Timeline
Completed

Started Nov 2015

Typical duration for phase_1

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

November 1, 2015

Completed
2 days until next milestone

First Submitted

Initial submission to the registry

November 3, 2015

Completed
2 days until next milestone

First Posted

Study publicly available on registry

November 5, 2015

Completed
2.4 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

March 19, 2018

Completed
5 months until next milestone

Study Completion

Last participant's last visit for all outcomes

August 2, 2018

Completed
Last Updated

September 25, 2018

Status Verified

September 1, 2018

Enrollment Period

2.4 years

First QC Date

November 3, 2015

Last Update Submit

September 21, 2018

Conditions

Outcome Measures

Primary Outcomes (1)

  • Number of participants with adverse events as a measure of safety and tolerability

    104 weeks (2 years)

Secondary Outcomes (4)

  • changes in urinary or plasma glycosaminoglycans (GAGs)

    104 weeks (2 years)

  • change in liver size

    104 weeks (2 years)

  • change in spleen size

    104 weeks (2 years)

  • change in levels of heparan sulfate and dermatan sulfate in the cerebrospinal fluid

    104 weeks (2 years)

Study Arms (1)

AGT-181

EXPERIMENTAL

AGT-181 (fusion protein of anti-human insulin receptor monoclonal antibody and alpha-L-iduronidase) administered once weekly x 26 weeks at same dose level as subject received in core study

Drug: AGT-181

Interventions

intravenous infusion over 3-4 hours

Also known as: HIRMAb-IDUA, fusion protein of monoclonal antibody to human insulin receptor fused to alpha-L-iduronidase
AGT-181

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Must have completed clinical trial AGT-181-102
  • Voluntary written consent by patient or legally responsible representative
  • All women of childbearing potential and sexually mature males must be advised to use a medically accepted method of contraception throughout the study.
  • Negative pregnancy test (females)

You may not qualify if:

  • Refusal to complete screening evaluations.
  • Any medical condition or other circumstances that may significantly interfere with study compliance
  • Patient is pregnant or lactating
  • Clinically significant spinal cord compression, evidence of cervical instability.
  • Subject developed clinically relevant hypersensitivity to AGT-181

Contact the study team to confirm eligibility.

Sponsors & Collaborators

MeSH Terms

Conditions

Mucopolysaccharidosis I

Interventions

valanafusp alpha

Condition Hierarchy (Ancestors)

MucopolysaccharidosesCarbohydrate Metabolism, Inborn ErrorsMetabolism, Inborn ErrorsGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesLysosomal Storage DiseasesMucinosesConnective Tissue DiseasesSkin and Connective Tissue DiseasesMetabolic DiseasesNutritional and Metabolic Diseases

Study Officials

  • Patrice Rioux, MD PhD

    ArmaGen, Inc

    STUDY DIRECTOR

Study Design

Study Type
interventional
Phase
phase 1
Allocation
NA
Masking
NONE
Masking Details
Open Label
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

November 3, 2015

First Posted

November 5, 2015

Study Start

November 1, 2015

Primary Completion

March 19, 2018

Study Completion

August 2, 2018

Last Updated

September 25, 2018

Record last verified: 2018-09