NCT02328482

Brief Summary

This will be a multi-center, randomized withdrawal, open-label, non-treatment concurrent control, parallel group study. Patients completing protocol BBCO-001 will be offered the opportunity to enter into this 12-month randomized withdrawal protocol.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
9

participants targeted

Target at below P25 for phase_3

Timeline
Completed

Started Jan 2015

Typical duration for phase_3

Geographic Reach
1 country

1 active site

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

December 25, 2014

Completed
6 days until next milestone

First Posted

Study publicly available on registry

December 31, 2014

Completed
1 day until next milestone

Study Start

First participant enrolled

January 1, 2015

Completed
2.8 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

October 1, 2017

Completed
2 months until next milestone

Study Completion

Last participant's last visit for all outcomes

December 1, 2017

Completed
Last Updated

July 17, 2019

Status Verified

February 1, 2018

Enrollment Period

2.8 years

First QC Date

December 25, 2014

Last Update Submit

July 15, 2019

Conditions

Outcome Measures

Primary Outcomes (2)

  • Change in disease markers

    long term effect of Cabaletta on disease progression as measured by the changes in the disease markers

    52 weeks

  • Change in swallowing quality of life

    long term effect of Cabaletta on disease progression as measured by the changes in the patient's swallowing quality of life

    52 weeks

Secondary Outcomes (1)

  • Long-term safety and tolerability of repeated intravenous (IV) of Cabaletta 30 g

    52 weeks

Study Arms (2)

Arm 1

EXPERIMENTAL

Trehalose 30 g for IV infusion administered every week over an additional 52 weeks

Drug: Tehalose 30gr

Arm 2

NO INTERVENTION

no-treatment concurrent control; follow-up over 52 weeks

Interventions

Trehalose 30 g for IV infusion administered every week over an additional 52 weeks

Also known as: Cabellta
Arm 1

Eligibility Criteria

Age18 Years - 80 Years
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Adult men and women who participated and completed study BBCO-001
  • Clinical and genetic diagnosis of OPMD
  • Able to provide written informed consent to participate in this study
  • Able to understand the requirements of the study and willing to comply with the requirements of the study

You may not qualify if:

  • Pregnant or lactating
  • Currently receiving anticoagulant treatment (e.g., warfarin)
  • Any life-threatening illness, medical condition or organ system dysfunction which, in the investigator's opinion, could compromise the subject's safety
  • Known hypersensitivity to any ingredient in the Cabaletta IV infusion
  • Currently participating in another clinical trial (other than BBCO-001) or have completed an interventional trial less than 30 days prior to the planned treatment start date

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

Montreal Neurological Institute, McGill University

Montreal, Quebec, H3A 2B4, Canada

Location

MeSH Terms

Conditions

Muscular DystrophiesMuscular Dystrophy, Oculopharyngeal

Condition Hierarchy (Ancestors)

Muscular Disorders, AtrophicMuscular DiseasesMusculoskeletal DiseasesNeuromuscular DiseasesNervous System DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Study Officials

  • Bernard Brais

    McGill University

    PRINCIPAL INVESTIGATOR

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

December 25, 2014

First Posted

December 31, 2014

Study Start

January 1, 2015

Primary Completion

October 1, 2017

Study Completion

December 1, 2017

Last Updated

July 17, 2019

Record last verified: 2018-02

Locations