NCT02244450

Brief Summary

Severe combined Immunodeficiencies ( SCID ) are a group of inherited diseases of the immune system by characterised profound abnormalities of T cell development . Infants with SCID require prompt clinical response to Prevent life -threatening infection and studies show significantly improved survival in babies Diagnosed at birth as a result of previous family history . SCID follows criteria for population -based newborn screening since it is asymptomatic at birth and fatal within the first year of life, the confirmation of the disease is easy, there is a curative treatment , and it is known that early stem cell transplantation improves survival . Quantification of TRECs (T- cell receptor excision circles ) in DNA extracted from Guthrie samples is a sensitive screening test for Specific and SCID . The investigators propose in this study to perform a neonatal screening of SCID , in a population of 200,000 babies over a period of two years . The investigators propose to study the clinical utility and cost effectiveness ratio, and SCID screening to demonstrate that could result in a broad benefit to Individuals detected , making screening relatively cost-effective in spite of the low incidence of the disease .

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
190,539

participants targeted

Target at P75+ for not_applicable

Timeline
Completed

Started Dec 2014

Longer than P75 for not_applicable

Geographic Reach
1 country

51 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

September 2, 2014

Completed
17 days until next milestone

First Posted

Study publicly available on registry

September 19, 2014

Completed
2 months until next milestone

Study Start

First participant enrolled

December 1, 2014

Completed
3.4 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

April 28, 2018

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

April 28, 2018

Completed
Last Updated

July 24, 2018

Status Verified

July 1, 2018

Enrollment Period

3.4 years

First QC Date

September 2, 2014

Last Update Submit

July 23, 2018

Conditions

Keywords

Neonatal screeningsevere combined immunodeficiencyT-cell Receptor Excision Circle

Outcome Measures

Primary Outcomes (1)

  • cost / efficiency ratio of the implementation of the generalized neonatal screening of SCID at birth

    Efficacy endpoint: number of children receiving early therapeutic suitable for curative ( transplant, enzyme treatment or gene therapy)

    18 months

Secondary Outcomes (7)

  • Cost / efficiency ratio of the implementation of the generalized neonatal screening of SCID at birth

    10 years

  • The cost of care during the first 18 months of life per child enjoying an early curative treatment in the first 4 months of life.

    18 months

  • Length of hospitalization of children with SCID in the first 18 months of life

    18 months

  • number of avoided deaths

    18 months

  • number of detected SCID patients

    18 months

  • +2 more secondary outcomes

Study Arms (2)

Screened patients

EXPERIMENTAL

SCID screening: more drops of blood are placed on a second Guthrie card when current screening (72 hours of life ) is performed after parents' information and consent. The card drawn for the protocol will follow the usual network except that the test for quantifying TRECs will be realized to determine the presence of SCID.

Biological: SCID screening

Control group

NO INTERVENTION

SCID children diagnosed without screening by pediatricians local referents DIP

Interventions

SCID screeningBIOLOGICAL
Screened patients

Eligibility Criteria

Age3 Days - 18 Months
Sexall
Healthy VolunteersYes
Age GroupsChild (0-17)

You may qualify if:

  • Screening Group: Newborn on day 3 of birth (premature and non premature)
  • Control group: Patients diagnosed with SCID without screening at participating centers

You may not qualify if:

  • Lack of parental consent
  • Children whose parents are adults under guardianship,
  • Children without health insurance, for the screening group:
  • The early exit of the child from the maternity hospital

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (51)

Angers Private Hospital Clinique de l'Anjou

Angers, France

Location

Angers University Hospital

Angers, France

Location

Argenteuil Hospital

Argenteuil, France

Location

Aulnay-sous-Bois Hospital CHI Robert Ballanger

Aulnay-sous-Bois, France

Location

Bordeaux Maison de Santé Protestante Bordeaux Bagatelle

Bordeaux, France

Location

Bordeaux Private Hospital Polyclinique Bordeuax Nord Aquitaine

Bordeaux, France

Location

Bordeaux University Hospital

Bordeaux, France

Location

Corbeil Essonnes Hospital Sud Francilien

Corbeil-Essonnes, France

Location

Créteil Hospital

Créteil, France

Location

Dijon University Hospital

Dijon, France

Location

Grenoble University Hospital

Grenoble, France

Location

Le Blanc Mesnil Private Hospital

Le Blanc-Mesnil, France

Location

Lens Hospital

Lens, France

Location

Libourne Maternity Hospital

Libourne, France

Location

Lille University Hospital

Lille, France

Location

Lormont Maternity Hospital Rive Droite

Lormont, France

Location

Lyon Maternity Hospital

Lyon, France

Location

Lyon University Hospital

Lyon, France

Location

Marseille Saint-Joseph Hospital

Marseille, France

Location

Marseille University Hospital La Conception

Marseille, France

Location

Marseille University Hospital Nord

Marseille, France

Location

Marseille University Hospital

Marseille, France

Location

Meaux Hospital

Meaux, France

Location

Montreuil Hospital CHI André Grégroie

Montreuil, France

Location

Nantes University Hospital

Nantes, 44000, France

Location

Nantes Private Hospital Clinique Jules Verne

Nantes, France

Location

Nantes University Hospital

Nantes, France

Location

Paris Hospital Saint-Joseph

Paris, France

Location

Paris Necker University Hospital

Paris, France

Location

Paris University Hospital Armand-Trousseau

Paris, France

Location

Paris University Hospital Bichat

Paris, France

Location

Paris University Hospital Bicêtre

Paris, France

Location

Paris University Hospital Béclère

Paris, France

Location

Paris University Hospital Jean Verdier

Paris, France

Location

Paris University Hospital La Pitié Salpétrière

Paris, France

Location

Paris University Hospital Louis Mourier

Paris, France

Location

Paris University Hospital Necker

Paris, France

Location

Poissy Hospital CHI Poissy-Saint-Germain

Poissy, France

Location

Pontoise Hospital René Dubos

Pontoise, France

Location

Rennes Private Hospital Clinique Mutualiste La Sagesse

Rennes, France

Location

Rennes University Hospital

Rennes, France

Location

Saint-Grégoire Private Hospital

Rennes, France

Location

Roubaix Hospital

Roubaix, France

Location

Saint-Herblain Private Hospital Polyclinique de l'Atlantique

Saint-Herblain, France

Location

Saint-Mande Army Hospital Begin

Saint-Mandé, France

Location

Saint-Martin-d'Hère Private Hospital Clinique Belledonne

Saint-Martin-d'Hères, France

Location

Strasbourg Private Hospital Clinique Adassa

Strasbourg, France

Location

Strasbourg University Hospital

Strasbourg, France

Location

Toulouse Private Hospital Clinique Sarrus Teinturiers

Toulouse, France

Location

Toulouse University Hospital P. DE VIGUIER

Toulouse, France

Location

Toulouse University Hospital

Toulouse, France

Location

Related Publications (2)

  • Thomas C, Durand-Zaleski I, Frenkiel J, Mirallie S, Leger A, Cheillan D, Picard C, Mahlaoui N, Riche VP, Roussey M, Sebille V, Rabetrano H, Dert C, Fischer A, Audrain M. Clinical and economic aspects of newborn screening for severe combined immunodeficiency: DEPISTREC study results. Clin Immunol. 2019 May;202:33-39. doi: 10.1016/j.clim.2019.03.012. Epub 2019 Apr 1.

  • Audrain MAP, Leger AJC, Hemont CAF, Mirallie SM, Cheillan D, Rimbert MGM, Le Thuaut AM, Sebille-Rivain VA, Prat A, Pinel EMQ, Divry E, Dert CGL, Fournier MAG, Thomas CJC. Newborn Screening for Severe Combined Immunodeficiency: Analytic and Clinical Performance of the T Cell Receptor Excision Circle Assay in France (DEPISTREC Study). J Clin Immunol. 2018 Oct;38(7):778-786. doi: 10.1007/s10875-018-0550-7. Epub 2018 Sep 24.

MeSH Terms

Conditions

Severe combined immunodeficiency, atypicalSevere Combined Immunodeficiency

Condition Hierarchy (Ancestors)

Primary Immunodeficiency DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesInfant, Newborn, DiseasesDNA Repair-Deficiency DisordersMetabolic DiseasesNutritional and Metabolic DiseasesImmunologic Deficiency SyndromesImmune System Diseases

Study Officials

  • Caroline THOMAS, MD

    Nantes University Hospital

    PRINCIPAL INVESTIGATOR
  • Marie AUDRAIN, MD

    Nantes University Hospital

    STUDY DIRECTOR
  • Sophie MIRALLIE

    Nantes University Hospital

    PRINCIPAL INVESTIGATOR

Study Design

Study Type
interventional
Phase
not applicable
Allocation
NON RANDOMIZED
Masking
NONE
Purpose
SCREENING
Intervention Model
PARALLEL
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

September 2, 2014

First Posted

September 19, 2014

Study Start

December 1, 2014

Primary Completion

April 28, 2018

Study Completion

April 28, 2018

Last Updated

July 24, 2018

Record last verified: 2018-07

Locations