NCT01971684

Brief Summary

The purpose of this study is to understand physician treatment decisions in selecting specific second line treatments in pediatric ITP and to determine the effectiveness of different second line ITP treatments. Eligible patients are those ages 1-18 years who are starting on a new second line treatment for ITP, defined as any treatment other than IVIG, steroids, anti-D globulin, or aminocaproic acid. Enrolled patients remain on the study for approximately one year.

Trial Health

90
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
120

participants targeted

Target at P50-P75 for all trials

Timeline
Completed

Started Aug 2013

Typical duration for all trials

Geographic Reach
2 countries

29 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

August 1, 2013

Completed
3 months until next milestone

First Submitted

Initial submission to the registry

October 21, 2013

Completed
8 days until next milestone

First Posted

Study publicly available on registry

October 29, 2013

Completed
3.4 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

April 1, 2017

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

April 1, 2017

Completed
Last Updated

May 21, 2020

Status Verified

May 1, 2020

Enrollment Period

3.7 years

First QC Date

October 21, 2013

Last Update Submit

May 19, 2020

Conditions

Keywords

ITPidiopathic thrombocytopenic purpurableeding scoreplatelet counthealth-related quality of lifeHRQLPurpuraPurpura, ThrombocytopenicPurpura, Thrombocytopenic, IdiopathicBlood Coagulation DisordersHematologic DiseasesHemorrhageSkin ManifestationsThrombocytopeniaBlood Platelet DisordersImmune System DiseasesHemorrhagic DisordersAutoimmune DiseasesTherapeutic Uses

Outcome Measures

Primary Outcomes (3)

  • change from baseline in patient reported outcomes

    Kids ITP Tool, Memorial Symptom Assessment Scale, Fatigue Scale

    Enrollment, 1 and 12 months

  • change from baseline in bleeding assessment

    ITP Bleeding Scale, Bleeding Assessment Tool

    Enrollment, 1, 6, and 12 months

  • change from baseline in platelet count

    over 1 year

Secondary Outcomes (1)

  • side effects and complications of treatments

    1 year

Study Arms (1)

Refractory Pediatric ITP Patients

Pediatric ITP patients, ages 1-18, starting a new second line ITP therapy, defined as not IVIG, steroids, anti-D, or aminocaproic acid.

Drug: Second Line ITP agents

Interventions

The treating physicians will select the second line agent and clinical data will be collected.

Also known as: rituximab, 6-mercaptopurine, mycophenolate mofetil, sirolimus, splenectomy, romiplostim, eltrombopag
Refractory Pediatric ITP Patients

Eligibility Criteria

Age1 Year - 18 Years
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64)
Sampling MethodNon-Probability Sample
Study Population

Pediatric refractory ITP patients starting on a new second line therapy

You may qualify if:

  • Immune Thrombocytopenia or Evans Syndrome
  • Ages \> 12 months to \<18 years
  • Starting a new second line therapy as defined as any therapy except IVIG, steroids, anti-D globulin, or aminocaproic acid
  • Starting a single agent/monotherapy

You may not qualify if:

  • Evans Syndrome with a history of or current evidence of autoimmune hemolytic anemia
  • Unwillingness to be followed for 1 year
  • Physician providing care is unwilling to participate
  • Patient is starting multiple second line agents simultaneously

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (29)

Arkansas Children's Hospital

Little Rock, Arkansas, 72202, United States

Location

Mattel Children's Hospital

Los Angeles, California, 90095, United States

Location

Children's Hospital of Oakland

Oakland, California, 94609, United States

Location

Children's Hospital of Orange County

Orange, California, 92868, United States

Location

Lucile Packard Children's Hospital

Palo Alto, California, 94304, United States

Location

UC Davis Medical Center

Sacramento, California, 95817, United States

Location

UCSF School of Medicine

San Francisco, California, 94143, United States

Location

Colorado Children's Hospital

Denver, Colorado, 80045, United States

Location

Children's Healthcare of Atlanta

Atlanta, Georgia, 30322, United States

Location

Ann & Robert H. Lurie Children's Hospital of Chicago

Chicago, Illinois, 60611, United States

Location

James Whitcomb Riley Hospital for Children

Indianapolis, Indiana, 46202, United States

Location

Boston Children's Hospital

Boston, Massachusetts, 02115, United States

Location

St. John Hospital & Medical Center

Detroit, Michigan, 48236, United States

Location

Goryeb Children's Hospital

Morristown, New Jersey, 07960, United States

Location

Columbia University Medical Center

New York, New York, 10032, United States

Location

New York-Presbyterian University Hospital of Columbia and Cornell

New York, New York, 10065, United States

Location

Duke University Medical Center

Durham, North Carolina, 27710, United States

Location

Cincinnati Children's Hospital

Cincinnati, Ohio, 45229, United States

Location

Nationwide Children's Hospital

Columbus, Ohio, 43205, United States

Location

Oregon Health and Sciences University

Portland, Oregon, 97239, United States

Location

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, 19104, United States

Location

Hasbro Children's Hospital

Providence, Rhode Island, 02903, United States

Location

St. Jude's Hospital

Memphis, Tennessee, 38105, United States

Location

University of Texas Southwestern Medical Center at Dallas

Dallas, Texas, 75235, United States

Location

Texas Children's Hospital

Houston, Texas, 77030, United States

Location

Seattle Children's

Seattle, Washington, 98105, United States

Location

McMaster Children's Hospital

Hamilton, Ontario, L8S 4K1, Canada

Location

Children's Hospital of Eastern Ontario

Ottawa, Ontario, KIH8L1, Canada

Location

U. de Montreal CHU St. Justine

Montreal, Quebec, H3T1C5, Canada

Location

Related Publications (2)

  • Grace RF, Shimano KA, Bhat R, Neunert C, Bussel JB, Klaassen RJ, Lambert MP, Rothman JA, Breakey VR, Hege K, Bennett CM, Rose MJ, Haley KM, Buchanan GR, Geddis A, Lorenzana A, Jeng M, Pastore YD, Crary SE, Neier M, Neufeld EJ, Neu N, Forbes PW, Despotovic JM. Second-line treatments in children with immune thrombocytopenia: Effect on platelet count and patient-centered outcomes. Am J Hematol. 2019 Jul;94(7):741-750. doi: 10.1002/ajh.25479. Epub 2019 Apr 29.

  • Grace RF, Despotovic JM, Bennett CM, Bussel JB, Neier M, Neunert C, Crary SE, Pastore YD, Klaassen RJ, Rothman JA, Hege K, Breakey VR, Rose MJ, Shimano KA, Buchanan GR, Geddis A, Haley KM, Lorenzana A, Thompson A, Jeng M, Neufeld EJ, Brown T, Forbes PW, Lambert MP. Physician decision making in selection of second-line treatments in immune thrombocytopenia in children. Am J Hematol. 2018 Jul;93(7):882-888. doi: 10.1002/ajh.25110. Epub 2018 May 6.

MeSH Terms

Conditions

Purpura, Thrombocytopenic, IdiopathicPurpuraPurpura, ThrombocytopenicBlood Coagulation DisordersHematologic DiseasesHemorrhageSkin ManifestationsThrombocytopeniaBlood Platelet DisordersImmune System DiseasesHemorrhagic DisordersAutoimmune Diseases

Interventions

RituximabMercaptopurineMycophenolic AcidSirolimusSplenectomyromiplostimeltrombopag

Condition Hierarchy (Ancestors)

Hemic and Lymphatic DiseasesThrombotic MicroangiopathiesCytopeniaPathologic ProcessesPathological Conditions, Signs and SymptomsSigns and Symptoms

Intervention Hierarchy (Ancestors)

Antibodies, Monoclonal, Murine-DerivedAntibodies, MonoclonalAntibodiesImmunoglobulinsImmunoproteinsBlood ProteinsProteinsAmino Acids, Peptides, and ProteinsSerum GlobulinsGlobulinsSulfhydryl CompoundsSulfur CompoundsOrganic ChemicalsPurinesHeterocyclic Compounds, 2-RingHeterocyclic Compounds, Fused-RingHeterocyclic CompoundsCaproatesAcids, AcyclicCarboxylic AcidsFatty AcidsLipidsMacrolidesLactonesSurgical Procedures, Operative

Study Design

Study Type
observational
Observational Model
COHORT
Time Perspective
PROSPECTIVE
Sponsor Type
OTHER
Responsible Party
PRINCIPAL INVESTIGATOR
PI Title
Principal Investigator, PKD Natural History Study

Study Record Dates

First Submitted

October 21, 2013

First Posted

October 29, 2013

Study Start

August 1, 2013

Primary Completion

April 1, 2017

Study Completion

April 1, 2017

Last Updated

May 21, 2020

Record last verified: 2020-05

Data Sharing

IPD Sharing
Will not share

Locations