NCT01340482

Brief Summary

The primary purpose of this study is to assess the safety and efficacy of repeated subcutaneous (SC) injections of KRN23 in adult subjects with X-Linked Hypophosphatemia (XLH). A Bone Substudy will evaluate the effects of single-blind KRN23 versus Placebo on bone mineral density and bone quality.

Trial Health

90
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
29

participants targeted

Target at P25-P50 for phase_1

Timeline
Completed

Started Apr 2011

Typical duration for phase_1

Geographic Reach
2 countries

6 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

April 1, 2011

Completed
14 days until next milestone

First Submitted

Initial submission to the registry

April 15, 2011

Completed
7 days until next milestone

First Posted

Study publicly available on registry

April 22, 2011

Completed
2 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

May 1, 2013

Completed
5 months until next milestone

Study Completion

Last participant's last visit for all outcomes

October 1, 2013

Completed
7.1 years until next milestone

Results Posted

Study results publicly available

October 26, 2020

Completed
Last Updated

June 18, 2024

Status Verified

June 1, 2024

Enrollment Period

2.1 years

First QC Date

April 15, 2011

Results QC Date

September 30, 2020

Last Update Submit

June 14, 2024

Conditions

Keywords

XLH

Outcome Measures

Primary Outcomes (1)

  • Safety and Efficacy of Repeated SC Injections of KRN23

    Safety and efficacy of repeated SC injections of KRN23 from baseline as assessed by serum phosphorus levels,immunogenicity, adverse events and clinically significant changes in vital signs and laboratory testing.

    On-Treatment: 6.5 months, 27 total visits

Secondary Outcomes (1)

  • Evaluation of Effect of Repeated SC Injections of KRN23

    On-Treatment: 6.5 months, 27 total visits

Other Outcomes (1)

  • Evaluation of Effect of Repeated SC Injections of KRN23 in Bone Substudy

    On-Treatment: 6.5 months, 27 total visits

Study Arms (1)

KRN23

EXPERIMENTAL

Escalating doses of KRN23 (0.05, 0.10, 0.30 and 0.60 mg/kg) will be administered SC every 28 days (up to 4 doses)

Drug: KRN23

Interventions

KRN23DRUG

Subjects will receive escalating doses of KRN23 administered by SC injections every 28-days (up to 4 doses) based on a dosing algorithm and discretion of the investigator and sponsor.

KRN23

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • years or older
  • Clinical diagnosis of XLH
  • TmP/GFR \< 2.0 mg/dL
  • GFR ≥60 mL/min
  • Corrected Ca \<10.8 mg/dL
  • A willingness to utilize adequate contraception and not become pregnant\[or to have their partner(s) become pregnant\] during the study

You may not qualify if:

  • Have any sign of active infectious disease or have had an infection requiring treatment with antibiotics within 3-weeks of Screening
  • History of known immunodeficiency
  • Pregnant or lactating females subjects or female planning to be become pregnant during the study
  • Receipt of a live (attenuated) vaccine (except for influenza vaccines) within 3-months of Screening, and/or during the study
  • Use of pharmacologic vitamin D metabolite or its analog, phosphate, calcimimetics, and ingestion of aluminum hydroxide antacids within 10-days prior to Screening and/or dosing
  • Use of any supplement containing phosphate, calcium and/or vitamin D within 10-days prior to Screening and/or dosing
  • Condition which could present a concern for either the subject's safety or difficulty with data interpretation

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (6)

University of California, San Francisco Medical Center

San Francisco, California, 94143, United States

Location

Yale University School of Medicine

New Haven, Connecticut, 06520, United States

Location

Clinical Research Center, Indiana University School of Medicine

Indianapolis, Indiana, 46202-5250, United States

Location

Duke Clinical Research Unit

Durham, North Carolina, 27710, United States

Location

University of Texas Health Science Center at Houston

Houston, Texas, 77030, United States

Location

Shriners Hospital for Children - Canada

Montreal, Quebec, H3G 1A6, Canada

Location

Related Publications (2)

  • Zhang X, Imel EA, Ruppe MD, Weber TJ, Klausner MA, Ito T, Vergeire M, Humphrey J, Glorieux FH, Portale AA, Insogna K, Carpenter TO, Peacock M. Pharmacokinetics and pharmacodynamics of a human monoclonal anti-FGF23 antibody (KRN23) in the first multiple ascending-dose trial treating adults with X-linked hypophosphatemia. J Clin Pharmacol. 2016 Feb;56(2):176-85. doi: 10.1002/jcph.570. Epub 2015 Aug 11.

  • Imel EA, Zhang X, Ruppe MD, Weber TJ, Klausner MA, Ito T, Vergeire M, Humphrey JS, Glorieux FH, Portale AA, Insogna K, Peacock M, Carpenter TO. Prolonged Correction of Serum Phosphorus in Adults With X-Linked Hypophosphatemia Using Monthly Doses of KRN23. J Clin Endocrinol Metab. 2015 Jul;100(7):2565-73. doi: 10.1210/jc.2015-1551. Epub 2015 Apr 28.

Related Links

MeSH Terms

Conditions

Familial Hypophosphatemic Rickets

Interventions

burosumab

Condition Hierarchy (Ancestors)

Rickets, HypophosphatemicRicketsBone Diseases, MetabolicBone DiseasesMusculoskeletal DiseasesHypophosphatemia, FamilialRenal Tubular Transport, Inborn ErrorsKidney DiseasesUrologic DiseasesFemale Urogenital DiseasesFemale Urogenital Diseases and Pregnancy ComplicationsUrogenital DiseasesMale Urogenital DiseasesMetal Metabolism, Inborn ErrorsMetabolism, Inborn ErrorsGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesMetabolic DiseasesNutritional and Metabolic DiseasesCalcium Metabolism DisordersHypophosphatemiaPhosphorus Metabolism DisordersVitamin D DeficiencyAvitaminosisDeficiency DiseasesMalnutritionNutrition Disorders

Limitations and Caveats

Only 2 subjects were randomized in and completed the bone substudy. Subsequently, the Sponsor terminated the bone substudy due to slow accrual.

Results Point of Contact

Title
Kyowa Kirin Pharmaceutical Development
Organization
Kyowa Kirin Pharmaceutical Development

Study Officials

  • Amy Zhang, PhD

    Kyowa Hakko Kirin Pharma, Inc.

    STUDY DIRECTOR

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
GT60
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 1
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

April 15, 2011

First Posted

April 22, 2011

Study Start

April 1, 2011

Primary Completion

May 1, 2013

Study Completion

October 1, 2013

Last Updated

June 18, 2024

Results First Posted

October 26, 2020

Record last verified: 2024-06

Locations