NCT01301898

Brief Summary

The purpose of this study is to evaluate the safety and efficacy of GC1111 (recombinant human iduronate-w-sulfatase) in Hunter Syndrome (Mucopolysaccharidosis II) patients

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
31

participants targeted

Target at P25-P50 for phase_1

Timeline
Completed

Started May 2010

Geographic Reach
1 country

1 active site

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

May 1, 2010

Completed
10 months until next milestone

First Submitted

Initial submission to the registry

February 22, 2011

Completed
1 day until next milestone

First Posted

Study publicly available on registry

February 23, 2011

Completed
6 days until next milestone

Primary Completion

Last participant's last visit for primary outcome

March 1, 2011

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

March 1, 2011

Completed
Last Updated

February 14, 2012

Status Verified

February 1, 2012

Enrollment Period

10 months

First QC Date

February 22, 2011

Last Update Submit

February 12, 2012

Conditions

Keywords

Hunter syndromeMPS IIIdursulfase

Outcome Measures

Primary Outcomes (1)

  • Primary Outcome

    measurement of % change of Urine GAG

    baseline, every 4 weeks

Secondary Outcomes (1)

  • Secondary Outcome

    baseline, every 12 weeks

Study Arms (3)

GC1111_0.5mg/kg

EXPERIMENTAL
Drug: GC1111_0.5mg/kg

GC1111_1.0mg/kg

EXPERIMENTAL
Drug: GC1111_1.0mg/kg

Elaprase_0.5mg/kg

ACTIVE COMPARATOR
Drug: Elaprase_0.5mg/kg

Interventions

GC1111_0.5mg/kg
GC1111_1.0mg/kg
Elaprase_0.5mg/kg

Eligibility Criteria

Age6 Years - 35 Years
Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64)

You may qualify if:

  • Patients with diagnosis of MPS II based on both clinical and biochemical criteria
  • Male, ages 6 to 35 years old
  • Patients who are able to comply with the study requirements
  • Patients who have given voluntary written consent to participate in the study
  • Patients who is acceptable for using an appropriate method of contraception

You may not qualify if:

  • History of a tracheostomy or a bone marrow transplant
  • Known hypersensitivity to idursulfase
  • Known shock to idursulfase
  • History of receiving treatment with another investigational therapy within the past 30 days
  • History of a stem cell transplant
  • Known hypersensitivity to any of the components of idursulfase
  • Female

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

Samsung Medical Center

Seoul, Irwon-dong, Gangnam-Gu, 135-710, South Korea

Location

Related Publications (1)

  • Sohn YB, Cho SY, Park SW, Kim SJ, Ko AR, Kwon EK, Han SJ, Jin DK. Phase I/II clinical trial of enzyme replacement therapy with idursulfase beta in patients with mucopolysaccharidosis II (Hunter syndrome). Orphanet J Rare Dis. 2013 Mar 18;8:42. doi: 10.1186/1750-1172-8-42.

MeSH Terms

Conditions

Mucopolysaccharidosis IISudden Infant Death

Condition Hierarchy (Ancestors)

X-Linked Intellectual DisabilityIntellectual DisabilityNeurobehavioral ManifestationsNeurologic ManifestationsNervous System DiseasesGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesHeredodegenerative Disorders, Nervous SystemMucopolysaccharidosesCarbohydrate Metabolism, Inborn ErrorsMetabolism, Inborn ErrorsLysosomal Storage DiseasesMucinosesConnective Tissue DiseasesSkin and Connective Tissue DiseasesMetabolic DiseasesNutritional and Metabolic DiseasesDeath, SuddenDeathPathologic ProcessesPathological Conditions, Signs and SymptomsInfant Death

Study Design

Study Type
interventional
Phase
phase 1
Allocation
RANDOMIZED
Masking
SINGLE
Who Masked
PARTICIPANT
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

February 22, 2011

First Posted

February 23, 2011

Study Start

May 1, 2010

Primary Completion

March 1, 2011

Study Completion

March 1, 2011

Last Updated

February 14, 2012

Record last verified: 2012-02

Locations