NCT01281189

Brief Summary

The purpose of this study is to determine whether dexpramipexole (150 mg twice daily) is safe and effective in the treatment of Amyotrophic Lateral Sclerosis (ALS).

Trial Health

98
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
942

participants targeted

Target at P75+ for phase_3

Timeline
Completed

Started Mar 2011

Geographic Reach
11 countries

82 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

January 20, 2011

Completed
1 day until next milestone

First Posted

Study publicly available on registry

January 21, 2011

Completed
1 month until next milestone

Study Start

First participant enrolled

March 1, 2011

Completed
1.7 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

November 1, 2012

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

November 1, 2012

Completed
8.6 years until next milestone

Results Posted

Study results publicly available

June 7, 2021

Completed
Last Updated

June 7, 2021

Status Verified

May 1, 2021

Enrollment Period

1.7 years

First QC Date

January 20, 2011

Results QC Date

December 4, 2020

Last Update Submit

May 10, 2021

Conditions

Keywords

Amyotrophic Lateral SclerosisALSMotor Neurone DiseaseMotor Neuron DiseaseLou Gehrig's disease

Outcome Measures

Primary Outcomes (3)

  • Composite Assessment of Function and Survival (CAFS) at 12 Months

    The Composite Assessment of Function and Survival (CAFS) is a between-group comparison of a single ranked clinical outcome based on (1) the change from baseline in ALS Functional Rating Scale-Revised (ALSFRS-R) score and (2) time to death. Each subject is ranked according to time-to-death (earlier deaths ranked lower than later deaths). Subjects who survive are ranked more favorably than subjects who died. Among the survivors, subjects are ranked according to change in ALSFRS-R (greater worsening of ALSFRS-R is ranked lower than less worsening or an improvement in ALSFRS-R). The ranked scores range from 001 to 941 (the number of subjects in the Efficacy Population) with larger rank score numbers associated with a better outcome. The ranks were analyzed using an ANCOVA model, which includes treatment as a fixed effect and adjusts for baseline ALSFRS-R score, duration of symptoms, site of onset, and use of riluzole. The least square mean rank score is presented for each treatment group.

    12 months

  • Death up to 12 Months (CAFs Individual Component)

    The longest duration of follow-up for this time to the death analysis was 12 months. In the study, subjects were followed for 12-18 months.

    12 months

  • Change From Baseline in ALSFRS-R at 12 Months (CAFs Individual Component)

    The ALSFRS-R (ALS functional rating scale with respiratory component) is a validated scale which measures 4 functional domains, comprising respiratory function, bulbar function, gross motor skills, and fine motor skills. There are a total of 12 questions, each scored from 0 to 4 for a total possible score of 48, with higher scores representing better function.

    12 months

Secondary Outcomes (3)

  • Death or Respiratory Insufficiency (DRI) up to Month 18

    18 months

  • Death up to 18 Months

    18 months

  • ≤50% Predicted Upright Slow Vital Capacity (SVC) or Died up to 18 Months

    18 months

Study Arms (2)

Dexpramipexole

EXPERIMENTAL
Drug: Dexpramipexole

Placebo

PLACEBO COMPARATOR
Drug: Placebo

Interventions

Oral tablet 150mg twice daily for up to 18 months.

Also known as: KNS-760704, BIIB050
Dexpramipexole

Oral tablet twice daily for up to 18 months.

Placebo

Eligibility Criteria

Age18 Years - 80 Years
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Aged 18 to 80 years old, inclusive, on Day 1.
  • Diagnosis of sporadic or familial ALS.
  • Onset of first ALS symptoms within 24 months prior to Day 1.
  • World Federation of Neurology El Escorial criteria are met for a possible, laboratory-supported probable, probable, or definite ALS diagnosis.
  • Upright slow vital capacity (SVC) of 65% or more at screening.
  • Patients taking or not taking Riluzole are eligible for this study: if a patient has never taken Riluzole, he or she is eligible; if a patient is currently taking Riluzole, he or she must have been on a stable dose for at least 60 days; if a patient has discontinued Riluzole, he or she must have stopped taking it for at least 30 days.
  • Must be able to swallow tablets at the time of study entry.

You may not qualify if:

  • Other medically significant illness.
  • Clinically significant abnormal laboratory values.
  • Pregnant women or women breastfeeding.
  • Prior exposure to dexpramipexole.
  • Currently taking pramipexole or other dopamine agonists.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (82)

Barrow Neurological Institute - St. Joseph's Hospital

Phoenix, Arizona, 85013, United States

Location

University of Arkansas for Medical Sciences

Little Rock, Arkansas, 72205, United States

Location

University of California at San Francisco - Fresno

Fresno, California, 93701, United States

Location

University of California, Irvine

Orange, California, 92868, United States

Location

University of California, Davis

Sacramento, California, 95817, United States

Location

California Pacific Medical Center

San Francisco, California, 94115, United States

Location

Hospital for Special Care

New Britain, Connecticut, 06053, United States

Location

Mayo Clinic - Jacksonville

Jacksonville, Florida, 32224, United States

Location

University of Miami Miller School of Medicine

Miami, Florida, 33136, United States

Location

University of South Florida Medical Center

Tampa, Florida, 33612, United States

Location

Emory University

Atlanta, Georgia, 30322, United States

Location

Northwestern University

Chicago, Illinois, 60611, United States

Location

Indiana University

Indianapolis, Indiana, 46202, United States

Location

University of Iowa

Iowa City, Iowa, 52242, United States

Location

University of Kansas Medical Center

Kansas City, Kansas, 66160, United States

Location

Johns Hopkins University School of Medicine

Baltimore, Maryland, 21287, United States

Location

Massachusetts General Hospital

Charlestown, Massachusetts, 02129, United States

Location

St. Mary's Health Care

Grand Rapids, Michigan, 49503, United States

Location

Hennepin County Medical Center

Minneapolis, Minnesota, 55404, United States

Location

Mayo Clinic - Rochester

Rochester, Minnesota, 55905, United States

Location

Washington University School of Medicine

St Louis, Missouri, 63110, United States

Location

Neurology Associates, P.C.

Lincoln, Nebraska, 68506, United States

Location

University of Nevada School of Medicine

Las Vegas, Nevada, 89102, United States

Location

Dartmouth-Hitchcock Medical Center

Lebanon, New Hampshire, 03756, United States

Location

Columbia University

New York, New York, 10032, United States

Location

Research Foundation of the State University of New York

Syracuse, New York, 12201, United States

Location

Carolinas Medical Center

Charlotte, North Carolina, 28207, United States

Location

Duke University Medical Center

Durham, North Carolina, 27705, United States

Location

Wake Forest University

Winston-Salem, North Carolina, 27157, United States

Location

The Cleveland Clinic Foundation

Cleveland, Ohio, 44195, United States

Location

Ohio State University

Columbus, Ohio, 43210, United States

Location

Providence ALS Center

Portland, Oregon, 97213, United States

Location

Penn State Hershey Medical Center

Hershey, Pennsylvania, 17033, United States

Location

ALS Center at Penn

Philadelphia, Pennsylvania, 19107, United States

Location

Drexel University College of Medicine

Philadelphia, Pennsylvania, 19129, United States

Location

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, 15213, United States

Location

Vanderbilt University Medical Center

Nashville, Tennessee, 37232, United States

Location

Texas Neurology

Dallas, Texas, 75214, United States

Location

Methodist Neurological Institute

Houston, Texas, 77030, United States

Location

University of Texas Health Sciences Center

San Antonio, Texas, 78229, United States

Location

University of Utah

Salt Lake City, Utah, 84132, United States

Location

University of Virginia Health System

Charlottesville, Virginia, 22908, United States

Location

University of Washington

Seattle, Washington, 98195, United States

Location

Prince of Wales Hospital

Randwick, New South Wales, Australia

Location

Westmead Hospital

Westmead, New South Wales, 2145, Australia

Location

Royal Brisbane and Women's Hospital

Herston, Queensland, 4029, Australia

Location

Calvary Health Care Bethlehem

Melbourne, Victoria, 3121, Australia

Location

AZ St-Lucas

Ghent, 9000, Belgium

Location

UZ Leuven

Leuven, 3000, Belgium

Location

Univ of Calgary / Foothills MC

Calgary, Alberta, T2V 1P9, Canada

Location

CHUM - Hopital Notre Dame

Montreal, Quebec, H2L 4M1, Canada

Location

Mcgill University

Montreal, Quebec, H3A 2B4, Canada

Location

London Health Sciences Centre

London, Canada

Location

Sunnybrook and Women's College and Health Sciences Centre

Toronto, M4N 3M5, Canada

Location

University of British Columbia

Vancouver, Canada

Location

CHRU de Lille - Hôpital Roger Salengro

Lille, 59037, France

Location

CHU de Limoges - Hôpital Dupuytren

Limoges, France

Location

Centre Hospitalier La Timone

Marseille, France

Location

CHU Gui de Chauliac

Montpellier, 34295, France

Location

CHU de Nice - Hôpital de l'Archet 1

Nice, France

Location

Hôpital La Pitié Salpétrière

Paris, 75013, France

Location

Charité - Universitätsmedizin Berlin

Berlin, Germany

Location

Bergmannsheil Gmbh

Bochum, Germany

Location

Medizinische Hochschule Hannover (MHH)

Hanover, Germany

Location

Universitätsklinikum Jena

Jena, Germany

Location

University of Ulm, RKU

Ulm, Germany

Location

Beaumont Hospital

Dublin, Dublin 9, Ireland

Location

Academisch Medisch Centrum

Amsterdam, 1105 AZ, Netherlands

Location

UMC St. Radboud

Nijmegen, 6525 GA, Netherlands

Location

Universitair Medisch Centrum Utrecht

Utrecht, 3584 CX, Netherlands

Location

Hospital Universitario de Bellvitge

Barcelona, 8907, Spain

Location

Hospital Vall d'Hebron

Barcelona, Spain

Location

Hospital La Paz

Madrid, 28046, Spain

Location

Hospital Carlos III

Madrid, Spain

Location

Sahlgrenska Universitetssjukhuset

Gothenburg, 41345, Sweden

Location

Karolinska Universitetssjukhuset, Solna

Stockholm, 17176, Sweden

Location

Queen Elizabeth Hospital

Birmingham, B15 2TH, United Kingdom

Location

Walton Centre for Neurology & Neurosurgery

Liverpool, L9 7LJ, United Kingdom

Location

Kings College Hospital NHS Foundation Trust

London, SE5 8AF, United Kingdom

Location

Newcastle University Hospital - Clinical Ageing Research Unit

Newcastle, NE4 5PL, United Kingdom

Location

John Radcliffe Hospital

Oxford, United Kingdom

Location

Sheffield Institute for Transnational Neuroscience

Sheffield, S10 2HQ, United Kingdom

Location

Related Publications (1)

  • Cudkowicz ME, van den Berg LH, Shefner JM, Mitsumoto H, Mora JS, Ludolph A, Hardiman O, Bozik ME, Ingersoll EW, Archibald D, Meyers AL, Dong Y, Farwell WR, Kerr DA; EMPOWER investigators. Dexpramipexole versus placebo for patients with amyotrophic lateral sclerosis (EMPOWER): a randomised, double-blind, phase 3 trial. Lancet Neurol. 2013 Nov;12(11):1059-67. doi: 10.1016/S1474-4422(13)70221-7. Epub 2013 Sep 23.

MeSH Terms

Conditions

Amyotrophic Lateral SclerosisMotor Neuron Disease

Interventions

Dexpramipexole

Condition Hierarchy (Ancestors)

Spinal Cord DiseasesCentral Nervous System DiseasesNervous System DiseasesNeurodegenerative DiseasesTDP-43 ProteinopathiesNeuromuscular DiseasesProteostasis DeficienciesMetabolic DiseasesNutritional and Metabolic Diseases

Intervention Hierarchy (Ancestors)

BenzothiazolesThiazolesAzolesHeterocyclic Compounds, 1-RingHeterocyclic CompoundsHeterocyclic Compounds, 2-RingHeterocyclic Compounds, Fused-Ring

Results Point of Contact

Title
Head of Regulatory
Organization
Knopp Biosciences

Study Officials

  • Merit Cudkowicz, MD, MSc

    Professor of Neurology of the Harvard Medical School

    PRINCIPAL INVESTIGATOR

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
OTHER
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

January 20, 2011

First Posted

January 21, 2011

Study Start

March 1, 2011

Primary Completion

November 1, 2012

Study Completion

November 1, 2012

Last Updated

June 7, 2021

Results First Posted

June 7, 2021

Record last verified: 2021-05

Locations